Genetic Test Details

Progressive external ophthalmoplegia (PEO) and Optic atrophy

Test Information

Titre
Progressive external ophthalmoplegia (PEO) and Optic atrophy
Catégorie
Mitochondrial
Sub Category
Mitochondrial nuclear gene
Gene/Platform/Region List
ACO2, AFG3L2, ALG3, ANTXR1, ATP1A3, AUH, C19orf12, C1QBP, CCDC88A, CISD2, CLN3, DGUOK, DNA2, DNAJC19, DNAJC30, DNM1L, DNMT1, FA2H, FDX2, FDXR, FH, GYG2, IBA57, ISCA2, KIF21A, KLC2, MECR, MFF, MFN2, MGME1, MICOS13, MTFMT, MTO1, MTPAP, MTRFR, NARS2, NDUFAF3, NDUFS1, NR2F1, OPA1, OPA3, PANK2, PDHX, PDSS1, PHOX2A, PLA2G6, PLP1, POLG, POLG2, PRPS1, RNASEH1, ROBO3, RRM2B, RTN4IP1, SLC19A2, SLC19A3, SLC25A4, SLC25A46, SLC52A2, SLC52A3, SNX10, SPG7, SUCLA2, TACO1, TCIRG1, TIMM8A, TK2, TMEM126A, TSFM, TUBB3, TUBB4A, TWNK, TYMP, UCHL1, WDR73, WFS1, YME1L1
Test type
Gene Panel
Samples Accepted
DNA , Dried Blood Spot , Blood
Indications
Carrier Cascade Testing , Diagnosis
Test Methodology
Sequencing
Methodology Notes
Augmented exome backbone
Disease/Condition
Progressive external ophthalmoplegia (PEO), Optic-nerve degeneration, Optic Atrophy

Dernière Mise à Jour: 18 juin 2025