Genetic Test Details

Maple Syrup Urine Disease

Test Information

Title
Maple Syrup Urine Disease
Category
Metabolic
Sub Category
Amino Acid Disorders
Gene/Platform/Region List
BCKDHA, BCKDHB, DBT, DLD
Test type
Gene Panel
Samples Accepted
DNA , Blood , Dried Blood Spot (accepted ONLY for exceptional circumstances)
Indications
Carrier Cascade Testing , Diagnosis
Test Methodology
Sequencing
Disease/Condition
Maple Syrup Urine Disease, BCKD Deficiency, Branched-Chain Ketoacid Dehydrogenase Deficiency, Maple Syrup Disease, MSUD

Last Updated: June 23, 2025