Genetic Test Details

Phenylketonuria

Test Information

Title
Phenylketonuria
Category
Metabolic
Sub Category
Amino Acid Disorders
Test type
Gene Panel
Samples Accepted
DNA , Blood , Dried Blood Spot (accepted ONLY for exceptional circumstances)
Indications
Carrier Cascade Testing , Diagnosis
Test Methodology
Sequencing
Methodology Notes
PAH, DNAJC12, GCH1, PCBD1, PTS, QDPR, SPR
Disease/Condition
Phenylketonuria, DNAJC12 Deficiency, GTP Cyclohydrolase Deficiency, DOPA-Responsive Dystonia, PCBD1 Deficiency, PTS Deficiency, QDPR Deficiency, Sepiapterin Reductase Deficiency

Last Updated: June 23, 2025